Huntington's disease


Disease modifying treatment available:
Time critical diagnosis and management:
Lateralising:


Aetiology

Huntington's disease is caused by a trinucleotide repeat expansion in the gene huntingtin (HTT).

Associated genes

Gene
HTT Search ClinVar Search ClinGen



Clinical features


Huntington's disease may cause the following:





Investigations


None


Laboratory Investigation Result

Treatment


No disease modifying treatment is available. The diagnosis should be made with genetic counselling given the implications for the individual and their families. Pre-implantation genetic diagnosis is available and allows individuals affected by the disease to ensure their offspring do not carry pathological variants.