Autoimmune encephalitis


Disease modifying treatment available:
Time critical diagnosis and management:
Lateralising:


Taxotomy

Subclassifications Epidemiology Clinical features
Anti-NMDA-receptor encephalitis Anti-NMDA-receptor encephalitis is thought to be the most common autoimmune encephalitis. The disorder has been reported to occur between the ages of 2 months and 85 years. Females are affected four times more commonly than males and the peak incidence is between 25 and 35. Dementia
Psychosis
Seizure
Anti-AMPA-receptor encephalitis In one case series of 22 people with anti-AMPA-receptor antibodies age at the time of diagnosis varied between 23 and 81 with the median age at diagnosis being 62. 64% of people had a tumour identified. Amnesia
Seizure
Psychosis
Anti-GABAA-receptor encephalitis None
Anti-GABAB-receptor encephalitis None
Anti-DPPX encephalitis None Weight loss
Diarrhoea
Myoclonus
Seizure
Tremor
Hyperekplexia
Amnesia
Cognitive impairment
Hallucination
Anti-mGluR1 cerebellar dysfunction None
Anti-mGluR5 encephalitis None
Anti-CASPR2 encephalitis CASPR2 associated autoimmunity is much more common in males than females. This may have something to do with expression of CASPR2 within the prostate. In a case series of 38 patients the median age of onset with 66 (https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4970662/). Myokymia
Seizure
Generalised pain
Insomnia
Weight loss
Cerebellar ataxia
Hyperhidrosis
Psychosis
Amnesia
Anti-dopamine receptor encephalitis None
Anti-neurexin 3α encephalitis None
Anti-IgLON5 disease None
Anti-LGI1 encephalitis None Focal seizure
Cognitive impairment
Facio-brachial dystonic seizures